A rare case of heterotaxy syndrome with agenesis of the head and uncinate process of the pancreas.

Merve Erol Gulseven; Emel Bostan; Perihan Ozkan Gumuskaya; Gulali Aktas; Suzan Deniz Onol; G�zde Konuk; Haluk Savli; Mehmet K���k

Abstract

A rare case of heterotaxy syndrome with agenesis of the head and uncinate process of the pancreas.

Heterotaxy syndrome is a rare complex syndrome characterized by cardiac and extra cardiac congenital malformations. The syndrome is divided into two main groups; right isomerism (Ivemark syndrome, asplenia) and left isomerism (polysplenia syndrome). Here we report a polysplenia syndrome with agenesis of head and uncinate process of the pancreas in a 52 year old woman who admitted to our clinic with complaints of weakness, lumbalgia, abdominal distention and constipation.

Author(s): Merve Erol Gulseven, Emel Bostan, Perihan Ozkan Gumuskaya, Gulali Aktas, Suzan Deniz Onol, Gözde Konuk, Haluk Savli, Mehmet Küçük
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